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Strain Name:

B6;129P2-Bace2tm1Bdes/J

Stock Number:

005618

Availability:

Repository-Cryopreserved


General Terms and Conditions

Genes & Alleles   Bace2;   Bace2tm1Bdes;


Product Information

Strain Details

Type JAX® GEMM® Strain - Mutant Stock
Additional information on JAX® GEMM® Strains.
Type JAX® GEMM® Strain - Mutant Strain
Type JAX® GEMM® Strain - Targeted Mutation
Specieslaboratory mouse
Donating Investigator Bart de Strooper,   KU Leuven and VIB

Strain Description
Mice that are homozygous for the targeted mutation are viable, fertile, normal in size and do not display any gross physical or behavioral abnormalities. Transcripts derived from the targeted locus do not contain exon 6. One of the enzyme's active sites is encoded by exon 6 so consequently, proteins generated from the targeted locus lack beta-secretase activity. This mutant mouse strain may be useful in studies of Alzheimer's disease.

Strain Development
A targeting vector containing a loxP site and hygromycin resistance gene flanked by FRT sites and was introduced into intron 5. A second loxP site was inserted within intron 6. The construct was electroporated into 129P2/OlaHsd derived E14 embryonic stem (ES) cells. Correctly targeted ES cells were injected into C57BL/6J blastocysts. The resulting chimeric animals were crossed to mice expressing Cre recombinase under the control of the phosphoglycerate kinase promoter to delete exon 6. Heterozygotes were bred to generate homozygotes.

Mammalian Phenotype Terms assigned by genotype

Bace2tm1Bdes/Bace2tm1Bdes

        involves: 129P2/OlaHsd * C57BL/6J
  • cellular phenotype
  • abnormal cell physiology (MGI Ref ID J:100925)
    • fibroblasts secrete higher levels of Abeta compared with wildtype cells, however no other abnormalities are seen and homozygotes are born at normal frequency, are fertile and healthy overall, and exhibit normal blood and clinical chemistry and pathological analysis

Gene & Allele Details

Allele Symbol Bace2tm1Bdes
Allele Name targeted mutation 1, Bart De Strooper
Common Name(s) BACE2delta6; Bace2tm1Psa;
Mutation Made By Bart de Strooper,   KU Leuven and VIB
Strain of Origin129P2/OlaHsd
ES Cell Line Strain129
Gene Symbol and Name Bace2, beta-site APP-cleaving enzyme 2
Chromosome 16
Gene Common Name(s) 1110059C24Rik; AEPLC; AI850424; ALP56; ARP1; ASP1; ASP21; BAE2; CDA13; CEAP1; DRAP; RIKEN cDNA 1110059C24 gene; expressed sequence AI850424;
Molecular Note Cre mediated recombination was used to remove exon 6 from the locus. [MGI Ref ID J:100925]

Control Information

  Control
   100492 B6129PF1/J
 
  Considerations for Choosing Controls

Genotyping Protocols

Bace2tm1Bdes

Colony Maintenance

Breeding & HusbandryWhen maintaining a live colony, these mice are bred as homozygotes.

Additional Web Information

Visit the Alzheimer's Disease Mouse Model Resource site for helpful information on Alzheimer's Disease and research resources.

Research Applications

This mouse can be used to support research in many areas including:

Mouse/Human Gene Homologs
Alzheimer's

Neurobiology Research
Alzheimer's Disease (Bace mutants)
Alzheimer's Disease

References

Selected Reference(s)

Dominguez D; Tournoy J; Hartmann D; Huth T; Cryns K; Deforce S; Serneels L; Camacho IE; Marjaux E; Craessaerts K; Roebroek AJ; Schwake M; D'Hooge R; Bach P; Kalinke U; Moechars D; Alzheimer C; Reiss K; Saftig P; De Strooper B. 2005. Phenotypic and biochemical analyses of BACE1- and BACE2-deficient mice. J Biol Chem 280(35):30797-806. [PubMed: 15987683]  [MGI Ref ID J:100925]

Additional References

Price and Supply Information

Strain Name: B6;129P2-Bace2tm1Bdes/J
Stock Number: 005618

Price Details

IMPORTANT NOTE: Prices are based on shipping destination. To view prices, select your shipping destination.

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Supply Details

Standard SupplyRepository-Cryopreserved. Must Be Recovered. Please refer to pricing and supply notes for further information.
Supply Notes Cryopreserved Embryos
This strain is also available as cryopreserved embryos from our Repository. Orders for cryopreserved embryos are supplied subject to a signed agreement that must be returned to the Customer Service Department after order placement. Experienced technicians at The Jackson Laboratory have recovered frozen embryos of this strain successfully. We will provide you enough embryos to perform two embryo transfers. The Jackson Laboratory does not guarantee successful recovery at your facility. For complete information on purchasing embryos from our repository, please visit our Cryopreserved Embryos web page.
Cryorecovery - Standard.
The recovery process begins when a signed agreement form is returned to the Customer Service Department after order placement. Although results vary by strain, at least two males and two females (two pairs) will be provided, typically within 15 weeks of our receipt of the signed agreement form. If the first recovery attempt is unsuccessful or only one pair is recovered, a second recovery will be done, extending the delivery time to approximately 25 weeks. At least one member of each pair will be of known genotype and will carry the mutation if it is a mutant strain. Please note that pairs may not reflect the mating scheme utilized by The Jackson Laboratory prior to cryopreservation of the strain. Mating schemes are sometimes modified for successful cryopreservation. Price represents a repository maintenance fee, which includes the cost of recovery of the strain from the cryopreservation resource and the periodic replacement of the frozen embryos used for recovery.

Cryorecovery to establish a Dedicated Supply for greater quantities of mice.
One to two pairs will be recovered to establish a Dedicated Supply of mice. Price by quotation. For more information on Dedicated Supply, please contact JAX® Services: Tel: 1-800-422-6423 or 1-207-288-5845; Email: jaxservices@jax.org.
This strain is included in the Induced Mutant Resource Colony collection.

LicensingSee General Terms and Conditions below for Licensing and Use Restrictions  
Control InformationView Control Information in Strain Details.

General Terms and Conditions

View JAX® Mice & Services Conditions of Use.

Effective September 26, 2007: License Requirements for Strains using Cre-lox Technology only apply in Canada, see Licenses for Strains using Cre-lox Technology.

For additional Licensing and Use Restrictions view the link(s) below:
- Use of MICE by companies or for-profit entities requires a license prior to shipping.

The Jackson Laboratory's Genotype Promise

The Jackson Laboratory has rigorous genetic quality control and mutant gene genotyping programs to ensure the genetic background of JAX® Mice strains as well as the genotypes of strains with identified molecular mutations. JAX® Mice strains are only made available to researchers after meeting our standards. However, the phenotype of each strain may not be fully characterized and/or captured in the strain data sheets. Therefore, we cannot guarantee a strain's phenotype will meet all expectations. To ensure that JAX® Mice will meet the needs of individual research projects or when requesting a strain that is new to your research, we suggest ordering and performing tests on a small number of mice to determine suitability for your particular project.
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